Case Reports
doi: 10.1007/s10545-006-0408-7.
Epub 2006 Nov 10.
Anakinra is safe and effective in controlling hyperimmunoglobulinaemia D syndrome-associated febrile crisis
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- PMID: 17103011
- DOI: 10.1007/s10545-006-0408-7
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Case Reports
Anakinra is safe and effective in controlling hyperimmunoglobulinaemia D syndrome-associated febrile crisis
J Inherit Metab Dis.
2006 Dec.
Abstract
Hyper-IgD and periodic fever syndrome (HIDS) is a hereditary autoinflammatory syndrome, characterized by recurrent inflammatory attacks. Treatment of HIDS is difficult. Recently, the IL-1ra analogue anakinra was reported to be successful in aborting the IgD inflammatory attacks in a vaccination model. We report a clinical case of spectacular reduction of febrile attacks in a severe HIDS patient.
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