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Case Reports
. 2022 May 10:43:102109.
doi: 10.1016/j.eucr.2022.102109. eCollection 2022 Jul.

Urachal rhabdomyosarcoma: A case report of an extremely rare localisation

Amina Karray  1 , Sondos Sahli  1 , Zohra Rahal  1 , Bochra Aziza  1 , Riadh Jouini  1
Affiliations
Case Reports

Urachal rhabdomyosarcoma: A case report of an extremely rare localisation

Amina Karray et al. Urol Case Rep. .

Abstract

Urachus is a tubular structure connecting the allatois to the bladder's apex, in the embryonic development. We report a rare case of a 5-year-old boy, with no past medical history, complaining of secondary enuresis, pollakiuria and urgent incontinence. Physical exam revealed a hypogastric mass. Echo guided percutaneous biopsy followed by a histological analysis showed embryonal RMS. The remainder of the staging ruled out metastasis. The patient received neoadjuvant chemotherapy before proceeding to complete tumor excision. Surgical exploration revealed that the tumor was primitively related to the urachus. Total resection was performed. The one year follow-up was uneventful.

Keywords: Oncology; Pediatrics; Rhabdomyosarcoma (RMS); Urachus.

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Conflict of interest statement

The authors declare that there are no conflicts of interest regarding the publication of this article.

Figures

Fig. 1
Fig. 1
Tumoral cells showed positive myogenic (a) desmin (b) markers in histopathology.
Fig. 2
Fig. 2
Pelvic MRI large anterior medial mass displacing the bladder.
See this image and copyright information in PMC

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