Skip to main page content
U.S. flag

An official website of the United States government

Dot gov

The .gov means it’s official.
Federal government websites often end in .gov or .mil. Before sharing sensitive information, make sure you’re on a federal government site.

Https

The site is secure.
The https:// ensures that you are connecting to the official website and that any information you provide is encrypted and transmitted securely.

Access keys NCBI Homepage MyNCBI Homepage Main Content Main Navigation
Case Reports
. 2016 Dec;35(10-12):524-528.
doi: 10.1080/15257770.2016.1184276.

Development of new forms of self-injurious behavior following total dental extraction in Lesch-Nyhan disease

Livia Gisbert de la Cuadra  1 , Rosa J Torres  2 , Luis M Beltrán  1 , Arantxa Sánchez  1 , Juan G Puig  1
Affiliations
Case Reports

Development of new forms of self-injurious behavior following total dental extraction in Lesch-Nyhan disease

Livia Gisbert de la Cuadra et al. Nucleosides Nucleotides Nucleic Acids. 2016 Dec.

Abstract

We report two Lesch-Nyhan Disease (LND) patients who developed new forms of self-injurious behavior following total dental extraction. Patients 1 and 2 were submitted to total teeth extraction at the age of 13 and 8 years, respectively, due to continuous self-biting, not prevented by mouth guards. Severity of dystonia was markedly reduced and quality of life improved. After 12 and 17 months, respectively, patient 1 started rubbing one foot against other and scratching toenails with his hands, and patient 2 stuck his legs and feet against hard objects. These forms of self-injury behavior could be easily prevented with protective materials, according to the mothers.

Keywords: HPRT; Lesch Nyhan; SIB.

PubMed Disclaimer

Similar articles

See all similar articles

Cited by

Publication types

LinkOut - more resources