Review
doi: 10.1177/0145445500242003.
A review of behavioral treatments used for Lesch-Nyhan syndrome
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- PMID: 10804680
- DOI: 10.1177/0145445500242003
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Review
A review of behavioral treatments used for Lesch-Nyhan syndrome
Behav Modif.
2000 Apr.
Abstract
Lesch-Nyhan syndrome is a genetic disorder resulting in hyperuricemia, choreoathetosis, mental retardation, and self-mutilation. The most salient feature of this disorder is the self-injurious behavior (SIB). Although the utility of behavioral interventions with SIB has been well documented, behavioral interventions with Lesch-Nyhan syndrome have been limited in number and long-term success. This article reviews the behavioral treatments that have been used in treating individuals with Lesch-Nyhan syndrome and discusses the strengths and weaknesses of these methods. Suggestions for future directions in the use of behavioral interventions for controlling SIB in Lesch-Nyhan syndrome are provided.
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